Phenylketonuria low protein diet

By | August 6, 2020

phenylketonuria low protein diet

The diet for PKU consists of a phenylalanine-free medical formula and carefully measured amounts of fruits, vegetables, bread, pasta, and cereals. Many people who follow a low phenylalanine phe food pattern eat special low protein breads and pastas. They are nearly free of phe, allow greater freedom in food choices, and provide energy and variety in the food pattern. Foods that contain large amounts of phe must be eliminated from a low phe diet. These foods are high protein foods, such as milk, dairy products, meat, fish, chicken, eggs, beans, and nuts. These foods cause high blood phe levels for people with PKU. This target is an easy way to visualize the foods allowed on the diet for PKU. As the foods get further away from the bull’s-eye, they are higher in phenylalanine. The foods outside the target are not included in the low-phenylalanine meal plan. It is not unusual for someone who follows a low phe diet to have 2 kinds of vegetables and a baked potato for dinner.

Attainment of protein growth and nutritional status. Future needs to optimize health for lhenylketonuria living keto diet infatile spasms PKU include specialized clinics for the management of metabolic disorders in adults and continued low to improve understanding of how PKU affects the progression of chronic disorders such pyenylketonuria cardiovascular disease and osteoporosis. Maintain regular communication between patient and dietitian. Keep a record of daily phenylalanine intake. Our bodies break down the protein in foods, phenylketonuria as meat and diet, into amino acids, which are the “building blocks” of protein. The profein phenylalanine that is tolerated, low more acceptable phenylketonuria diet will be, protein it will ease the practical and social burden that the diet demands. How is PKU tested? Page last reviewed: 3 December Next review due: 3 December Nuts, peas, and diet and products made from these foods.

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Metrics details. Phenylketonuria PKU is an autosomal recessive inborn error of phenylalanine metabolism caused by deficiency in the enzyme phenylalanine hydroxylase that converts phenylalanine into tyrosine. This manuscript is a supplement containing the practical application of the dietary treatment. This handbook can support dietitians, nutritionists and physicians in starting, adjusting and maintaining dietary treatment. Phenylketonuria PKU is an autosomal, recessive, genetic disorder. It is caused by a deficiency of the enzyme phenylalanine hydroxylase which normally converts phenylalanine to tyrosine. Deficiency of this enzyme leads to an increased production of phenylketone bodies hence phenylketonuria and accumulation of phenylalanine resulting in high phenylalanine levels in the blood and brain. A strict, lifelong low phenylalanine diet is the principle treatment in PKU. It may be the only treatment or used in combination with drug treatments.

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